Moyamoya Disease, Moyamoya Disease

In fact, the name derives from its angiographic image; the "puff of smoke," which is how moyamoya loosely translates from Japanese, refers to the appearance of multiple compensatorily dilated striate vessels seen on angiography. Contrast-enhanced T1-weighted images are better than FLAIR images for depicting the leptomeningeal ivy sign in Moyamoya disease. MRI and MRA should be performed for the diagnosis and follow-up of Moyamoya disease. Diffusion-weighted imaging can also be used for following the clinical course of children with Moyamoya disease, in whom new focal deficits are highly suspicious of new infarcts.

Conventional angiography provided the conclusive diagnosis of Moyamoya disease in most cases and should be performed before any surgical considerations.

Source: Wikipedia > Moyamoya Disease